{"id":1703,"date":"2022-09-06T12:50:00","date_gmt":"2022-09-06T10:50:00","guid":{"rendered":"https:\/\/epilepsiarussi.com\/blog\/?p=1703"},"modified":"2023-03-27T14:50:50","modified_gmt":"2023-03-27T12:50:50","slug":"sindrome-lennox-gastaut-lgs","status":"publish","type":"post","link":"https:\/\/www.epilepsiarussi.com\/blog\/sindrome-lennox-gastaut-lgs\/","title":{"rendered":"S\u00edndrome Lennox-Gastaut (LGS)"},"content":{"rendered":"\n<figure class=\"wp-block-image size-large\"><a href=\"https:\/\/www.epilepsiarussi.com\/blog\/wp-content\/uploads\/2023\/03\/Sindrome-Lennox-Gastaut-min.png\"><img decoding=\"async\" loading=\"lazy\" width=\"1024\" height=\"576\" src=\"https:\/\/www.epilepsiarussi.com\/blog\/wp-content\/uploads\/2023\/03\/Sindrome-Lennox-Gastaut-min-1024x576.png\" alt=\"\" class=\"wp-image-1753\" srcset=\"https:\/\/www.epilepsiarussi.com\/blog\/wp-content\/uploads\/2023\/03\/Sindrome-Lennox-Gastaut-min-1024x576.png 1024w, https:\/\/www.epilepsiarussi.com\/blog\/wp-content\/uploads\/2023\/03\/Sindrome-Lennox-Gastaut-min-300x169.png 300w, https:\/\/www.epilepsiarussi.com\/blog\/wp-content\/uploads\/2023\/03\/Sindrome-Lennox-Gastaut-min-768x432.png 768w, https:\/\/www.epilepsiarussi.com\/blog\/wp-content\/uploads\/2023\/03\/Sindrome-Lennox-Gastaut-min-1536x864.png 1536w, https:\/\/www.epilepsiarussi.com\/blog\/wp-content\/uploads\/2023\/03\/Sindrome-Lennox-Gastaut-min-500x281.png 500w, https:\/\/www.epilepsiarussi.com\/blog\/wp-content\/uploads\/2023\/03\/Sindrome-Lennox-Gastaut-min.png 1920w\" sizes=\"(max-width: 1024px) 100vw, 1024px\" \/><\/a><\/figure>\n\n\n\n<p>En el blog y en la web del Instituto hemos hablado a menudo sobre el denominado <strong>S\u00edndrome de Lennox-Gastaut<\/strong> (<strong>LGS<\/strong>) pero dado que sigue siendo un tema recurrente sobre el que recibimos m\u00faltiples consultas, hoy hemos pedido al Dr. Russi que nos resumiera los puntos m\u00e1s relevantes sobre dicho S\u00edndrome: \u00bfa qu\u00e9 edad se diagnostica? \u00bfcu\u00e1les son sus causas? posibles tratamientos.<\/p>\n\n\n\n<p>Resumimos por escrito los puntos que trata el <strong>Dr. Antonio Russi<\/strong> en el v\u00eddeo. Deseamos les sea de utilidad.<\/p>\n\n\n\n<!--more-->\n\n\n\n<p><em>El <strong>S\u00edndrome Lennox-Gastaut<\/strong> es un S\u00edndrome de inicio temprano: normalmente suele manifestarse a los 2 o 3 a\u00f1os.<\/em><\/p>\n\n\n\n<p><em>Presenta m\u00faltiples tipos de crisis epil\u00e9pticas:<\/em><\/p>\n\n\n\n<ul>\n<li><em>Crisis de tipo t\u00f3nica: de contractura<\/em><\/li>\n\n\n\n<li><em>Crisis at\u00f3nicas: con ca\u00edda<\/em><\/li>\n\n\n\n<li><em>Ausencias<\/em><\/li>\n\n\n\n<li><em>Crisis focales o tambi\u00e9n con sacudidas o mioclonias<\/em><\/li>\n<\/ul>\n\n\n\n<p><em>El S\u00edndrome Lennox-Gastaut presenta un EGG t\u00edpico que consiste en el registro de una descarga o varias descargas de punta onda lenta y tambi\u00e9n durante el sue\u00f1o descargas de alucinaciones de alta frecuencia.<\/em><\/p>\n\n\n\n<p><em>El s\u00edndrome Lennox- Gastaut lleva asociado retraso psicomotor severo.<\/em><\/p>\n\n\n\n<h2><strong><em>Or\u00edgen<\/em><\/strong> del S\u00edndrome Lennox- Gastaut<\/h2>\n\n\n\n<p><em>Las causas son varias:<\/em><\/p>\n\n\n\n<p><em>Una bastante frecuente puede ser debido a complicaciones durante el parto tales como accidentes vasculares tipo infarto cerebral o hemorragia cerebral, enfermedades metab\u00f3licas, encefalitis y\/o mutaciones gen\u00e9ticas.<\/em><\/p>\n\n\n\n<p><em>Su origen puede tambi\u00e9n hallarse en alteraciones de los cromosomas, las denominadas cromosomopat\u00edas.<\/em><\/p>\n\n\n\n<h2>\u00bfC\u00f3mo diagnosticar el LGS? <\/h2>\n\n\n\n<p><em>Para realizar un diagn\u00f3stico preciso del <strong>S\u00edndrome de Lennox-Gastaut<\/strong> recomendamos realizar una evaluaci\u00f3n diagn\u00f3stica de laboratorio y que la misma se complemente con una resonancia magn\u00e9tica cuyo resultado nos permitir\u00e1 comprobar si hay lesiones estructurales .<\/em><\/p>\n\n\n\n<h2>Tratamiento farmacol\u00f3gico<\/h2>\n\n\n\n<p><em>El tratamiento es dif\u00edcil dado que es una epilepsia farmacorresistente. Como medicamentos para tratar el s\u00edndrome recomendamos probar inicialmente \u00e1cido valproico, carbamazepina, clonazepam , levetiracetam, lamotrigina, y los dem\u00e1s medicamentos que suelen utilizarse en epilepsias farmacoresistentes. Es complejo sin conocer el caso en concreto determinar por qu\u00e9 medicamento empezar, sobre todo teniendo en cuenta que actualmente disponemos de m\u00e1s de 20 f\u00e1rmacos para tratar las crisis epil\u00e9pticas.<\/em><\/p>\n\n\n\n<p><em>Destacar que ensayos cl\u00ednico recientes indican que &nbsp;tambi\u00e9n el <a href=\"https:\/\/epilepsiarussi.com\/blog\/sinergia-terapeutica-del-clobazam-cbd-combinado-con-cannabidiol-cbd-en-el-tratamiento-del-sindrome-de-dravet-y-lennox-gastaut\/\"><strong>cannabidiol<\/strong><\/a> &nbsp;ha dado buen resultado para el tratamiento del S\u00edndrome Lennox-Gastaut.<\/em><\/p>\n\n\n\n<h2><em>Cirug\u00eda para tratar el S\u00edndrome Lennox-Gastaut<\/em> &#8211; LGS<\/h2>\n\n\n\n<p><em>La cirug\u00eda es sobre todo recomendable para los casos en los que se manifiesten crisis de ca\u00eddas que pueden comportar accidentes graves. La cirug\u00eda prescrita para estos casos ser\u00eda la denominada <strong>callosotom\u00eda<\/strong> que generalmente es parcial si bien tambi\u00e9n puede ser total.<\/em><\/p>\n\n\n\n<p><em>La callosotom\u00eda consiste en desconectar los dos lados del cerebro para que las descargas epil\u00e9pticas no provoquen ca\u00eddas al paciente. Dicha cirug\u00eda consiste en separar los dos hemisferios que se hallan unidos a trav\u00e9s del puente o conexi\u00f3n denominada Cuerpo Calloso.<\/em><\/p>\n\n\n\n<p><em>Ser\u00eda tambi\u00e9n aconsejable en aquellos casos en los que se aprecie accidentes vasculares importantes con infartos y con hemiparesia de un lado y epilepsia en el otro lado. Estos casos suelen operarse operarse con cirug\u00eda abierta, la denominada craneotom\u00eda.<\/em><\/p>\n\n\n\n<p><em>Otras alternativas de tratamiento ser\u00edan contemplar la posibilidad de seguir una <strong><a href=\"https:\/\/www.epilepsiarussi.com\/es\/epilepsia-tratamiento\/alternativo\">dieta cetog\u00e9nica<\/a><\/strong> o realizar <strong>estimulaci\u00f3n vagal<\/strong>. &nbsp;<\/em><\/p>\n\n\n\n<figure class=\"wp-block-embed is-type-video is-provider-youtube wp-block-embed-youtube wp-embed-aspect-16-9 wp-has-aspect-ratio\"><div class=\"wp-block-embed__wrapper\">\n<iframe loading=\"lazy\" title=\"FAQS sobre S\u00edndrome Lennox-Gastaut\" width=\"584\" height=\"329\" src=\"https:\/\/www.youtube.com\/embed\/30uNyCf7eq8?feature=oembed\" frameborder=\"0\" allow=\"accelerometer; autoplay; clipboard-write; encrypted-media; gyroscope; picture-in-picture; web-share\" allowfullscreen><\/iframe>\n<\/div><\/figure>\n","protected":false},"excerpt":{"rendered":"<p>Preguntas frecuentes sobre el S\u00edndrome de Lennox-Gastaut <a href=\"https:\/\/www.epilepsiarussi.com\/blog\/sindrome-lennox-gastaut-lgs\/\">Sigue leyendo <span class=\"meta-nav\">&rarr;<\/span><\/a><\/p>\n","protected":false},"author":1,"featured_media":1753,"comment_status":"open","ping_status":"closed","sticky":false,"template":"","format":"standard","meta":[],"categories":[20,7,325,322,284],"tags":[45],"yoast_head":"<!-- This site is optimized with the Yoast SEO plugin v19.14 - https:\/\/yoast.com\/wordpress\/plugins\/seo\/ -->\n<title>Tratamiento y causas del S\u00edndrome Lennox-Gastaut - LGS<\/title>\n<meta name=\"description\" content=\"El S\u00edndrome Lennox-Gastaut (LGS) es un tipo de Epilepsia Rara que se da en edad temprana. 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